Intact atrial septum (IAS), occurring in ~10% of patients with hypoplastic left heart syndrome (HLHS), conveys significant neonatal morbidity and mortality. Perinatal interventions have been described, but outcomes remain poor. We present a fetus with HLHS-IAS who underwent immediate novel postnatal atrial appendage anastomosis achieving rapid left atrial decompression.

JACC: Case Reports Editor-in-Chief 

Julia Grapsa, MD, PhD, FACC

CME Editor 

Nadeen N. Faza, MD, FACC

Authors
Chau P. Nguyen, MD

Important Dates

Date of Release: September 7, 2022
Term of Approval/Date of CME/MOC/ECME Expiration: September 6, 2023